[Absent right superior vena cava with left superior vena cava draining to an unroofed coronary sinus].
نویسندگان
چکیده
We describe the case of a 1-month-old infant with a complete atrioventricular septal defect with right dominance, situs solitus, and drainage from the persistent left superior vena cava to the coronary sinus. Corrective surgery was carried out without previous cardiac catheterization. During the operation, the right superior vena cava was found to be absent. Cyanosis and head-and-neck edema were observed in the immediate postoperative period. Transthoracic echocardiography carried out after injection of a small volume of stirred saline into an epicranial vein demonstrated the presence of microbubbles in the left cardiac cavities. A second operation was performed to prevent drainage from the left superior vena cava to the left atrium (via the unroofed coronary sinus) and to insert a PTFE conduit between the innominate vein and the right atrial appendage. The outcome was excellent. In this report, the embryological, clinical, diagnostic and therapeutic characteristics of this entity are discussed.
منابع مشابه
Occlusion of persistent left superior vena cava to unroofed coronary sinus using vena cava filter and coils.
A 48 year old female with complex cyanotic heart disease and pulmonary hypertension was partly cyanosed because of a persistent left superior vena cava draining into an unroofed coronary sinus. The left superior vena cava, which measured 22 mm in diameter, was successfully occluded with a Günther Tulip Vena Cava Mreye Filter which acted as a barrier for embolisation coils.
متن کاملRepair of truncus arteriosus with intact ventricular septum (Van Praagh type B2) in a neonate.
superior vena cava draining into the left atrium with absent right superior vena cava. Ann Thorac Surg 1971;11:160-4. 4. Quaegebeur J, Kirklin JW, Pacifico AD, Bargeron LM Jr. Surgical experience with unroofed coronary sinus. Ann Thorac Surg 1979;27:418-25. 5. Chiu IS, Hegerty A, Anderson RH, de Leval M. The landmarks to the atrioventricular conduction system in hearts with absence or unroofing...
متن کامل[Cardiac transplantation in a patient with a persistent left superior vena cava and an absent right superior vena cava].
Persistent left superior vena cava is the most common congenital venous abnormality of the thorax and has a prevalence of 0.5% among the general population.1 Other related malformations include absent right superior vena cava and presence of a left azygos vein. In these situations, the right side of the head and the right arm drain mainly through the innominate vein in the left superior vena ca...
متن کاملIncidentally Detected Persistent Left Superior Vena Cava With an Absent Right Superior Vena Cava in a Neonate
A 3-week-old female underwent transthoracic echocardiography (iE33, Philips medical system, Andover, MA, USA) to evaluate a grade 1 systolic murmur. In the subcostal view, blood flow in the inferior vena cava drained to the right atrium, while no blood flow from the superior vena cava to the right atrium was noted (Figure 1A). In the four-chamber view, no superior vena caval blood flow was seen...
متن کاملPersistent left superior vena cava draining into left atrium, unroofed coronary sinus, and coronary sinus atrial septal defect as rare cause for severe right heart dilatation: diagnostic steps and therapy.
. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . doi:10.1093/ehjci/jet261 Online publish-ahead-of-pr...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- Revista espanola de cardiologia
دوره 58 8 شماره
صفحات -
تاریخ انتشار 2005